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Description of
Handbook of Tumor Syndromes
Tumors/cancers are characterized by uncontrolled growths of abnormal cells that extend beyond their usual boundaries and disrupt the normal functions of affected organs and systems. While about 75%80% of tumors/cancers arise sporadically without a family connection, 20%25% appear to be familial (including 10%15% nonhereditary familial tumors [or familial tumors] and 5%10% hereditary familial tumors [or hereditary tumors]). As nonhereditary and hereditary familial tumors often show both tumor-related and non-tumor-related (or syndromic) symptoms, they are referred to as tumor syndromes (or cancer susceptibility syndromes).